СИНДРОМ ПОДОВЖЕНОГО ІНТЕРВАЛУ QT У ПРАКТИЦІ ПЕДІАТРА
DOI:
https://doi.org/10.32782/2226-2008-2024-4-11Ключові слова:
синдром подовженого інтервалу QT, синдром раптової cерцевої смерті, каналопатії, тахікардія типу «пірует», діти.Анотація
Мета роботи – представити сучасний погляд на проблему синдрому подовженого інтервалу QT (LQTS) у дітей, що дозволить своєчасно попереджувати розвиток раптової серцевої смерті в дитячому віці та проілюструвати тактику ведення хворого з LQTS власним клінічним спостереженням. У роботі наведено огляд сучасної літератури щодо причин та механізмів розвитку, діагностики та лікування LQTS у дітей. Представлено власне клінічне спостереження підлітка з LQTS та тактику його ведення. Викладені матеріали дозволять розширити знання лікарів-педіатрів про LQTS як предиктора фатальних порушень ритму серця у дітей та дадуть можливість своєчасно попереджувати розвиток раптової серцевої смерті в дитячому віці.
Посилання
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